3-Hydroxyacyl-CoA Dehydrogenase II Deficiency: Introduction
3-Hydroxyacyl-CoA Dehydrogenase II Deficiency: A rare genetic disorder involving the deficiency of an enzyme (hydroxyacyl-coa dehydrogenase).
Acyl-CoA Dehydrogenase Deficiency, Short-Chain
SCAD Deficiency
SCADH Deficiency
Lipid-Storage Myopathy Associated with SCAD Deficiency
SCAD Deficiency, Congenital (Generalized)
SCAD Deficiency, Adult-Onset (Localized) ...
Long Chain Acyl-CoA Dehydrogenase Deficiency
ACADL
LCAD Deficiency
Nonketotic Hypoglycemia Caused by Deficiency of Acyl-CoA Dehydrogenase
VLCAD ...
Short chain acyl-CoA dehydrogenase (SCAD) deficiency is a rare autosomal recessive genetic disorder of fatty acid catabolism belonging to a group of diseases known as fatty acid oxidation disorders (FOD).
Medium chain acyl-CoA dehydrogenase deficiency: a disorder in which babies can't burn fat when they run out of glucose. It can cause physical problems.
Very long-chain acyl-CoA dehydrogenase functions within mitochondria, the energy-producing centers in cells. This enzyme is abundant in the heart and certain muscles, where it plays a key role in supplying energy.
MCADD see Medium Chain Acyl-CoA Dehydrogenase Deficiency
McArdle disease see Glycogen Storage diseases
McCune-Albright syndrome
McLeod Neuroacanthocytosis syndrome see Neuroacanthocytosis disorders
McLeod syndrome see Neuroacanthocytosis disorders ...
MCAD stands for medium-chain acyl-CoA dehydrogenase. Children born with MCAD deficiency cannot metabolize (digest) medium-chain fats such as coconut oil. If undiagnosed, the disorder can lead to metabolic collapse, coma and even death.
Carnitine uptake deficiency
Long-chain L-3-hydroxyacyl-CoA dehydrogenase deficiency
Medium-chain acyl-CoA dehydrogenase (MCAD) deficiency
Trifunctional protein deficiency
Very long-chain acyl-CoA dehydrogenase deficiency (VLCAD) ...
This gene provides instructions for making an enzyme called short-chain acyl-CoA dehydrogenase, which is required to break down (metabolize) a group of fats called short-chain fatty acids.
One such disorder is medium chain acyl-CoA dehydrogenase deficiency, which prevents the baby from properly processing fatty acids.
medium chain acyl-CoA dehydrogenase deficiency
This disorder of fatty acid oxidation can cause sudden death in infancy and serious disabilities in survivors, such as mental retardation.
 See also: Deficiency, Symptom, Diabetes, Myopathy, Cancer
  
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