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Aganglionosis

Disease AgammaglobulinemiaAge-related cognitive decline

Aganglionosis- total intestinal
Overview
A developmental defect of the intestinal tract where the muscles of the intestines are unable to function and move food along the digestive tract.

 


Aganglionosis, colonic
absence of normal ganglia causing failure of normal colonic movement of faeces, presenting clinically with constipation or failure to pass meconium.

Aganglionosis of myenteric plexus of colon, functional obstruction, aganglionic segment of normal calibre, continuous involvement, from rectum proximally, males (80%), usually presents by 6 weeks, complications: enterocolitis, perforation, ...

Aganglionosis, total intestinal ... intestinal blockage
Aggressive NK-cell leukaemia ... enlarged spleen
Aggressive systemic mastocytosis ... ascites, enlarged spleen
Agranulocytosis ... anal ulcers
Aicardi-Goutieres syndrome 1 ... enlarged spleen ...

Hirschsprung disease is also called aganglionosis, congenital aganglionic megacolon, congenital intestinal aganglionosis, and megacolon.
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Feel Wiped Out Working Odd Hours? ...

aganglionosis/Hirschsprung's Disease
intestinal atresia
pseudo-obstruction
microvillus inclusion
malabsorption
tumor
trauma (injury to these organs)
massive resection of the intestine
mesenteric thrombosis ...

Occasionally, infants with ultra-short segment aganglionosis have only mild or intermittent constipation, often with intervening bouts of mild diarrhea, resulting in delay in diagnosis.

(Congenital Megacolon; Colonic Aganglionosis)
by Michelle Badash, MS
En Español (Spanish Version) ...

(Congenital Megacolon; Colonic Aganglionosis)
by Michelle Badash, MS
Definition ...

Chemiluminescent Immunoassay; Chymotrypsin Inhibitor Activity; Colony-inhibiting Activity; Congenital Intestinal Aganglionosis
CVT
Cardiovascular Technologist; Central Venous Temperature; Cerebral Venous Thrombosis; Congenital Vertical Talus ...

Aganglionosis see Hirschsprung disease
Agenesis of the Corpus Callosum
AGS see Aicardi-Goutières syndrome
Agyria see Cortical malformations
AHC see Alternating Hemiplegia of Childhood
AHO see Albright Hereditary Osteodystrophy ...

intestinal aganglionosis
Intestinal Lipodystrophy
Intestinal Lipophagic Granulomatosis
Intestinal Lymphangiectasia
Intestinal Lymphangiectasis
Intestinal Polyposis III
Intestinal Pseudoobstruction ...

See also: Symptom, Surgery, Anemia, Neuropathy, Colitis

Disease AgammaglobulinemiaAge-related cognitive decline

 
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