Angiomatosis- diffuse corticomeningeal- of Divry and Van Bogaert
Overview
A rare condition characterized by diffuse sclerosis and clusters of capillaries in parts of the brain as well as a marbled appearance to the skin.
Angiomatosis - A diseased state of the vessels with the formation of multiple angiomas.
Anomaly - An irregularity or deviation from normal; an abnormal structure.
Ascites - An accumulation of serous fluid in the abdominal cavity.
Bacillary angiomatosis is a re-emerging bacterial infection that is identical or closely related to one which commonly afflicted thousands of soldiers during World War I.
Bacillary angiomatosis is so characteristic today of AIDS that it is an AIDS defining disease, according to the CDC (Centers For Disease Control).
bacillary angiomatosis
Type: Term
Definitions:
1. an infection of immunocompromised patients by a newly recognized bacterium, Bartonella henselae, characterized by fever, granulomatous cutaneous nodules, and peliosis hepatis in some cases.
Bacillary angiomatosis is a systemic disease described by Stoler and associates in 1983. There are unusual cutaneous papules and nodules distinct from Kaposi sarcoma.
Angiomatosis
an abnormality of blood vessels characterized by the formation of many angiomas. For a general description, see angiomatosis. Numerous varieties of angiomatosis are known, with terminology reflecting tissue composition.
Alternate Names : Encephalotrigeminal angiomatosis
Definition
Sturge-Weber syndrome is a rare disorder that is present at birth. A child with this condition will have a port-wine stain birthmark (usually on the face) and neurologic problems.
Retinoblastoma
Retinoblastoma Treatment (PDQ®): Treatment - Health Professional Information [NCI]
Retinoblastoma Treatment (PDQ®): Treatment - Patient Information [NCI]
Retinocerebellar Angiomatosis ...
Angiomatosis retinae
Cerebelloretinal Angiomatosis, Familial
Hippel-Lindau Disease
VHL syndrome
von Hippel-Lindau Disease ...
Haemangiomatosis of the skeletal system with or without involvement of the overlying skin, resulting in osteolysis and fibrous replacement of bone.
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Lymphangiomatosis
Pulmonary Langerhans' cell granulomatosis (histiocytosis)
Sarcoidosis ...
Angioma, angiomatosis, anti-convulsants, buphthalmos, convulsions, epilepsy, glaucoma, hemiaropia, hemiplegia, neurological disorder, port-wine stain, status epilepticus, Sturge Weber syndrome.
Bacillary angiomatosis
Bacterial cellulitis
Basal cell carcinoma
Bazex's syndrome (see paraneoplastic acrokeratosis of Bazex)
Becker's nevus
Bed bugs
Behçet's syndrome
Benign familial chronic pemphigus
Benign mucosal pemphigoid ...
Bacillary angiomatosis
Candidiasis
Cytomegalovirus infection
Cryptococcal infection
Cryptosporidium enterocolitis (or other protozoal infections)
Mycobacterium avium complex (MAC) infection ...
Bacillary angiomatosis
Erythromycin 500 mg once daily x 3 months; or doxycycline 100 mg twice daily x 3 months
AII ...
Bacillary angiomatosisA bacterial infection due to a cat scratch most often seen today in people with HIV.
Synonym(s): Angiomatosis
Table of Contents (click to jump to sections)
What is Von Hippel-Lindau Disease (VHL)?
Is there any treatment?
What is the prognosis?
What research is being done?
Clinical Trials
Organizations ...
Encephalotrigeminal angiomatosis
Causes
The cause of Sturge-Weber is unknown. It is not thought to be passed down (inherited) through families.
Diffuse Neonatal Hemangiomatosis (0 images)
Diffuse Plane Xanthoma (0 images)
Digitus Mortuus (0 images)
Diphtheria (0 images)
Discoid Lupus Erythematosus (DLE) (55 images)
Disseminated Cicatricial Pemphigoid (0 images) ...
Encephalofacial Angiomatosis
Encephalopathy, Fatal Infantile, With Olivopontocerebellar Hyperplasia
Encephalopathy, Hypoglycemic
Encephalotrigeminal Angiomatosis
Enchondromatosis
Enchondromatosis with Multiple Cavernous Hemangiomas ...
Meningeal Capillary Angiomatosis
Meningeal Fibroblastoma
Meningioma
Meningitis
Meningitis
Meningitis (Bacterial), Antibiotics for - Medication
Meningitis, Bacterial
Meningitis, Meningococcal
Meningitis, Tuberculous ...
In persons with HIV/AIDS the disease (usually called bacillary angiomatosis) can cause severe inflammation of the brain, bone marrow, lymph nodes, lungs, spleen and liver. The disease can be fatal in persons with HIV.
The abnormal growth of blood vessels into tumors is called angiomatosis, and it makes the tumors difficult to treat because of the ample blood supply. Surgery is an option for some tumors, as is radiation.
Vision problems (retinal angiomatosis)
Headaches, signs of elevated intracranial pressure, and trouble walking (cerebellar hemangioblastoma)
Blood Vessels in the Retina of the Eye
Less common findings include: ...
Bartonella henselae : A species of gram-negative bacteria that is the etiologic agent of bacillary angiomatosis (ANGIOMATOSIS, BACILLARY). This organism can also be a cause of CAT-SCRATCH DISEASE in immunocompetent patients. [1]
Other HON resources ...
Doxycycline, ciprofloxacin, or erythromycin for bacillary angiomatosis (see below)
Aminoglycosides for Encephalitis (brain infection)
The overwhelming majority of children with this disease do very well, and have no permanent complications.
A rare, genetic multisystem disorder characterized by the abnormal growth of tumors in certain parts of the body (angiomatosis).
Osler-Weber-Rendu Syndrome is a rare disorder that is genetic, via autosomal dominant inheritance. It is also known as hereditary haemorrhagic telangiectasia, Rendu-Osler-Weber syndrome, familial hemorrhagic angiomatosis, Osler disease, ...
Kaposiform hemangioendothelioma
Tufted angioma
Cutaneovisceral angiomatosis with thrombocytopenia (CAT) also called multifocal lymphangioendotheliomatosis with thrombocytopenia (MLT) ...
Babies may develop a type of hepatic hemangioma called benign infantile hemangioendothelioma (also called multinodular hepatic hemangiomatosis). This rare, noncancerous tumor has been linked to high rates of heart failure and death in infants.
Unraveling Mysteries Associated with Cat-Scratch Disease, Bacillary Angiomatosis, and Related Syndromes. Emerging Infectious Diseases Journal. January-March 1995, Volume 1, Number 1.
Diffuse neonatal hemangiomatosis ... premature birth, stillbirth
Digitalis -- Teratogenic Agent ... fetal death
Digitorenocerebral syndrome ... stillbirth
Digoxin -- Teratogenic Agent ... fetal death
Diphallus -- rachischisis -- imperforate anus ...
Liver hemangioma; Hemangioma of the liver; Cavernous hepatic hemangioma; Infantile hemangioendothelioma; Multinodular hepatic hemangiomatosis
Treatment:
Most cavernous hepatic hemangiomas are treated only if there is persistent pain.
Parinaud’s oculoglandular syndrome: eye infection that causes inflammation of the optic nerve and can lead to blindness
Bacillary angiomatosis: systemic illness characterized by lesions on the skin, mucosal surfaces, liver, ...
Cat scratch disease: An overview based on a study of 1,200 patients. ... Cat scratch disease, bacillary angiomatosis, and other infections due to Rochalimaea. ...
Full article ...
Pneumocystis carinii pneumonia, "PCP pneumonia," now called Pneumocystis jiroveci pneumonia
Candida esophagitis -- painful yeast infection of the esophagus
Bacillary angiomatosis -- skin lesions caused by a bacteria called Bartonella, ...
Bacillary angiomatosis. Rarely seen in people not infected with HIV, this infection first appears as purplish to bright red patches on your skin.
Multinodular hepatic hemangiomatosis
Multiple Endocrine Neoplasia (MEN) II
Multiple Endocrine Neoplasia (MEN) I
Multiple lentigines syndrome
Multiple lipoprotein-type hyperlipidemia
Multiple myeloma
Multiple sclerosis
Multiple system atrophy ...
 See also: Angioma, Cancer, Fever, Sclerosis, Deficiency
  
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