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Dentinogenesis imperfecta

Disease Dentin dysplasiaDentistry

Dentinogenesis Imperfecta Type III
National Organization for Rare Disorders, Inc.
Synonyms ...

 


Brandywine Type Dentinogenesis Imperfecta
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Dentinogenesis Imperfecta Type III
Dentinogenesis Imperfecta, Shields Type
Dento-Oculo-Osseous Dysplasia
Denys-Drash Syndrome
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AMI, RIS, IMB, ODE, Defecation, Dentinogenesis Imperfectas, Deoxyriboviruses, Icosahedral Cytoplasmic, dextro Amphetamine, Disease, Otorhinolaryngological, DNA Transposable Elements, Dopamine, Dosages, Radiotherapy, Ethics Consultation, Genes, fos, ...

pearl, Macrodontia, Microdontia, Taurodontism) - disturbances in tooth formation (Dilaceration, Regional odontodysplasia, Turner's hypoplasia) - other hereditary disturbances in tooth structure (Amelogenesis imperfecta, Dentinogenesis imperfecta, ...

Dentinogenesis imperfecta, an autosomal dominant disorder, causes abnormal dentin that is dull bluish brown and opalescent and does not cushion the overlying enamel adequately. Such teeth cannot withstand occlusal stresses and rapidly become worn.

General practitioner's radiology case 89. Dentinogenesis imperfecta. SADJ. 2011 Feb;66(1):33… more…
Whole-Exome Sequencing Identifies… ...

Additional features of these conditions can include blue sclerae, short stature, hearing loss, respiratory problems, and a disorder of tooth development called dentinogenesis imperfecta.

See also: Injuries, Cancer, Osteoporosis, Dysplasia, Deficiency

Disease Dentin dysplasiaDentistry

 
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