Dietary Fructose Intolerance
Department of Food and Nutrition Services,
University of Iowa Hospitals and Clinics
Peer Review Status: Internally Peer Reviewed
Creation Date: May 2004
Last Revision Date: May 2004 ...
Hereditary fructose intolerance is a disorder in which a person lacks the protein needed to break down fructose. Fructose is a fruit sugar that naturally occurs in the body.
Fructose intolerance - the inability to break down fructose, which is a type of simple sugar found in fruits, fruit juices, sugar (for example, cane sugar) and certain vegetables.
Fructose Intolerance, Hereditary Causes, Symptoms And Treatment And Related Disorders
There are three inherited disorders of fructose metabolism that are recognized and characterized.
Hereditary fructose intolerance (HFI) . Also known as Fructose-1-Phosphate Aldolase Deficiency , Fructosemia Disorder. An inherited inability to digest fructose (fruit sugar) or its precursors (sugar, sorbitol and brown sugar).
Hereditary fructose intolerance may be relatively mild or a very severe disease. Complete avoidance of fructose and sucrose produces good results in most children with this condition. A few children will go on to develop severe liver disease.
Hereditary fructose intolerance: Treatment
(Professional Guide to Diseases (Eighth Edition)) ...
Hereditary fructose intolerance
Hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu syndrome)
Hereditary motor and sensory neuropathy (Charcot-Marie-Tooth disease)
Hereditary nephritis (Alport syndrome)
Hereditary ovalocytosis ...
Lactose intolerance - Glycogen storage disease (type I, type II, type III, type IV, type V, type VI, type VII) - fructose metabolism (Fructose intolerance, Fructose bisphosphatase deficiency, Essential fructosuria) - galactose metabolism ...
11, Energy Resources Conservation, Equipment and Supplies, Fructose Intolerances, Glycosylasparaginase, Health Problem, International, Helicopter, Emergency, Hydatid Cyst, Hepatic, Idiopathic Multicentric Osteolyses, Illusion, Kinesthetic, ...
Fructose 1-phosphate aldolase (aldolase B) deficiency: This deficiency causes the clinical syndrome of hereditary fructose intolerance. Inheritance is autosomal recessive; incidence is estimated at 1/20,000 births.
Fructose intolerance: an under-recognized problem. Am J Gastroenterol 2003; 98:1348.
Suarez FL, Furne JK, Springfield J, Levitt MD. Bismuth subsalicylate markedly decreases hydrogen sulfide release in the human colon. Gastroenterology 1998; 114:923.
Definition Hereditary fructose intolerance is a metabolic disorder in which the small intestine cannot process fructose (fruit sugar) into a source of energy because of an enzyme deficiency that prevents fructose absorption.
Carbohydrate disorders; examples include diabetes insipidus, hereditary fructose intolerance, galactosemia, pyruvate metabolism disorders, von Gierke’s disease, McArdle disease, Pompe’s disease, and Forbes’ disease ...
AllRefer Health - Inborn Errors of Metabolism (Branched Chain Ketoaciduria - Nutritional Considerations, Fructose Intolerance - Nutritional Considerations, Galactosemia - Nutritional Considerations, ...
There are may causes of watery diarrhea, including carbohydrate malabsorption such as lactose, sorbitol, and fructose intolerance, intestinal infections or Irritable Bowel Syndrome.
Neonatal iron storage disease
Certain metabolic disorders such as tyrosinemia and galactosemia
Fructose intolerance
Familial erythrophagocytic histiocytosis
Peroxisomal diseases
Defects in respiratory chain and fatty acid oxidation.
For instance, cystinosis galactosemia, glycogen storage disease, hereditary fructose intolerance, Lowe syndrome, Wilson disease, tyrosinemia, medullary cystic disease, and vitamin D dependency, have been shown to cause Fanconi syndrome.
18. Choi YK, Kraft N, Zimmerman B, et al. Fructose intolerance in IBS and utility of fructose-restricted diet. J Clin Gastroenterol 2008;42:233-8.
Serious illnesses such as kidney failure, liver disease or heart problems
Insulinoma
Hereditary fructose intolerance
Hormonal deficiencies
Early stages of pregnancy
Prolonged fasting
Long periods of strenuous exercise ...
Cystinosis
Drugs such as ifosfamide (a chemotherapy drug), outdated tetracycline, or acetazolamide
Fanconi Syndrome
Inherited fructose intolerance
Wilson's disease ...
can also result from inherited disorders that disrupt the body's normal breakdown and use of nutrients. Examples include the rare disease cystinosis, in which cystine crystals are deposited in bones and other tissues; hereditary fructose intolerance; ...
celiac disease prevents the small intestine from doing its work. The disease is more common in people of European heritage. The only cure is a gluten-free diet. Similar symptoms may occur with lactose (milk) intolerance or fructose intolerance.
Frontonasal Dysplasia
Frostbite
Frozen Shoulder
Fructose Intolerance, Hereditary
Fructose or Sorbitol Intolerance
Fructose-1-Phosphate Aldolase Deficiency
Fructosemia
Fructosuria
Fryns Syndrome ...
 See also: Symptom, Deficiency, Diabetes, Cancer, Hereditary fructose intolerance
  
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