Hemophagocytic lymphohistiocytosis

Hemophagocytic lymphohistiocytosis: A rare, cancer-like disorder in which both histiocytes and lymphocytes start to proliferate and attack body tissues or organs.

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hemophagocytic lymphohistiocytosis HLH. A rare disorder in which histiocytes and lymphocytes (types of white blood cells) build up in organs including the skin, spleen and liver, and destroy other blood cells.

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This proliferation of immune cells often causes a life-threatening reaction called hemophagocytic lymphohistiocytosis. Hemophagocytic lymphohistiocytosis causes fever, destroys blood-producing cells in the bone marrow, and damages the liver.

Patients with ALCL may present with signs and symptoms consistent with hemophagocytic lymphohistiocytosis.[36] There is a subgroup of ALCL with leukemic peripheral blood involvement.

Disorders of the macrophage/monocytoid lineages include Rosai Dorfman disease and hemophagocytic lymphohistiocytosis. Malignant disorders include malignant histiocytosis (histiocytic sarcoma) and the monocytic or myelomonocytic leukemias.

See also: Histiocytosis, Cancer, Lymphoma, Viral, Symptom