Primary ciliary dyskinesia |
   |
Primary ciliary dyskinesia: The immotile cilia syndrome, a condition in which poorly functioning cilia (hairlike projections from cells) in the respiratory tract contribute to retention of secretions and recurrent infection.
Primary Ciliary Dyskinesia Causes, Symptoms and Treatment and Related Disorders ...
What is primary ciliary dyskinesia?
Primary ciliary dyskinesia is a disorder characterized by chronic respiratory tract infections, abnormally positioned internal organs, and the inability to have children (infertility).
Primary Ciliary Dyskinesia
Figure A shows the organs that primary ciliary dyskinesia can affect. Figure B shows a cross-section of the trachea (windpipe). Figure C shows a closeup view of normal cilia lining the trachea.
Primary ciliary dyskinesia
History of repeated respiratory infections, and frequent sinusitis
Chest CT (characteristic findings include hyperinflation, peribronchial thickening, atelectasis, bronchiectasis, situs inversus) ...
"Genetic Causes of Bronchiectasis: Primary Ciliary Dyskinesia" (in English). Respiration 72 (3): 252-63. PMID 17534128.
^ Dalrymple-Hay MJ, Lucas J, Connett G, Lea RE (1999).
Primary Ciliary Dyskinesia
Primary CNS Lymphoma Treatment (PDQ®): Treatment - Health Professional Information [NCI]
Primary CNS Lymphoma Treatment (PDQ®): Treatment - Patient Information [NCI]
Primary Failure Adrenocortical Insufficiency ...
Primary Ciliary Dyskinesia
Primary Focal Dystonia see Dystonia
Primary Immunodeficiencies
Primary Lateral Sclerosis see Motor Neurone disease
Primary Progressive Aphasia see Frontotemporal Lobar Degeneration including Frontotemporal Dementia ...
For example, a condition called primary ciliary dyskinesia affects the cilia so they do not beat correctly to clear the mucus. Cystic fibrosis is another condition that affects the lungs and causes bronchiectatic airways.
Primary ciliary dyskinesia impairs the ability small hairs called cilia to clear mucus and bacteria from the airways. Recurrent lung infections can occur and cause bronchiectasis.
Alpha-1 Antitrypsin Deficiency or Anomaly.
Primary ciliary dyskinesia is a disorder in which the lung's cilia are not functioning properly. The cilia are little 'hairs' on the inside of a bronchus which sweep mucous up towards the trachea. In this disorder the cilia are 'immotile' i.e.
Cystic fibrosis causes about a third of all bronchiectasis cases in the United States. Certain genetic conditions can also cause bronchiectasis, including primary ciliary dyskinesia and immunodeficiency syndromes.
It can occur secondary to anatomic birth defects of the lung, as well as in diseases such as cystic fibrosis, Young's syndrome, primary ciliary dyskinesia, allergic bronchopulmonary aspergillosis, immunodeficiency conditions, ...
Abnormalities of local immunological and nonimmunological defence mechanisms are important, especially in children; cystic fibrosis sinonasal manifestation, primary ciliary dyskinesia and IgA deficiency are the best known inherited diseases ...
Mammaplasties, Metabolic Activation, Monocrotaline Hydrochloride (13alpha,14alpha)-Isomer, NSC 95441, Oatp-C Transport Protein, Oils, Commercial, Urine Concentrating Ability, Pacemaker, Biological, Pre-Ictal Memory Loss, Primary Ciliary Dyskinesias, ...
These can include such varied disorders as cystic fibrosis, cigarette smoking induced chronic obstructive pulmonary disease, primary ciliary dyskinesia, tracheal or bronchial malacia, foreign body aspiration, vocal cord dysfunction, ...
 See also: Dyskinesia, Infections, Cough, Fibrosis, Cystic fibrosis
|
RSS
