Proteus syndrome: A disturbance of cell growth including benign tumors under the skin, overgrowth of the body, often more on one side than the other (hemihypertrophy), and overgrowth of fingers (macrodactyly).
The syndrome is named after the greek god proteus the polymorphous who could change his appearance. The elephant man (john merrick) of 19th century england who was thought to have had neurofibromatosis probably had proteus syndrome.
Proteus syndrome is characterised by overgrowth of many tissues affecting multiple sites on both sides of the body. The overgrowth may affect the skin (the epidermal naevus), blood vessels, fat, fibrous tissue, lungs, kidneys and other organs.
Overgrowth may occur with idiopathic Hemihypertrophy, Beckwith Wiedemann syndrome, Klippel Trenaunay syndrome, lymphangioma, neurofibromatosis type 1 or proteus syndrome.
Proteus syndrome
Prothrombin Gene Mutation see Hereditary Thrombophilia
Proximal Focal Femoral Deficiency see Lower Limb Abnormalities
Prune Belly syndrome
Pseudo Hurler Polydystrophy see Mucopolysaccharide diseases and Associated diseases ...
Adenolipomatosis
Lipodystrophia progressive
Madelung's syndrome (multiple symmetrical lipomatosis)
Neurofibromatosis
Proteus syndrome
Weber-Christian disease ...
Later examinations of his case and even his skeleton have led experts to determine he probably had a mysterious disease called Proteus Syndrome.
Hamartomas are benign (noncancerous) tumor-like growths. Other conditions that are part of the PTEN hamartoma tumor syndrome are Bannayan-Riley-Ruvalcaba syndrome, Proteus syndrome, and Proteus-like syndrome.
Examples of overgrowth syndromes include neurofibromatosis, Sotos syndrome, Beckwith-Wiedemann syndrome, Simpson-Golabi-Behmel syndrome, Weaver syndrome, Proteus syndrome, Sturge-Weber syndrome and fragile X syndrome.
Montagu suggested in his book The Elephant Man: A Study in Human Dignity that Merrick suffered Neurofibromatosis type 1, and this has continued to be reported. Although, careful research has shown that Merrick actually suffered from Proteus syndrome ...
Emery-Dreifuss Type, Nerve Disease, Peripheral, Urological Diagnostic Technics, Vomiting, Postoperative, Painful Menstruations, Partner, Domestic, Periodicals Publishing, Dental, Personnel, Health, phage f2, Enterobacteria, Phytase, Proteus Syndrome, ...
Proteus Syndrome
Protoporphyria
Proximal Muscular Dystrophy
PRP
PRS
Prune Belly Syndrome
Pruritus (PDQ®): Supportive care - Health Professional Information [NCI]
Pruritus (PDQ®): Supportive care - Patient Information [NCI] ...
Proteus Syndrome (9 images)
Prurigo Actinica (0 images)
Prurigo Gestationis (0 images)
Prurigo Nodularis Hyde (6 images)
Prurigo Pigmentosa (0 images)
Prurigo Simplex Chronica (1 images)
Prurigo Simplex Subacuta (1 images) ...
 See also: Cancer, Fibromatosis, Neurofibroma, Neurofibromatosis, Lymphoma
  
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