Sensorineural deafness
Definition
Sensorineural deafness is hearing loss that occurs from damage to the inner ear, the nerve that runs from the ear to the brain (auditory nerve), or the brain.
Sensorineural deafness : Definition
Sensorineural deafness : Common Causes
Sensorineural deafness : Pictures & Images
Ear anatomy ...
Can sensorineural deafness and male infertility be inherited?
Sensorineural deafness and male infertility is inherited in an autosomal recessive pattern, which means both copies of chromosome 15 in each cell have a deletion.
Sensorineural deafness Treatment
Review Date: 06/12/2009
Reviewed By: Luc Jasmin, MD, PhD, Department of Neurosurgery and Gene Therapeutics Research Institute, Cedars-Sinai Medical Center, Los Angeles, CA.
Albinism ocular late onset sensorineural deafness
Overview
Ocular albinism (OA) is an inherited disorder characterized by partial or complete absence of pigment in the eyes.
Sensorineural deafness
Sensorineural deafness means the sound waves are transmitted to the inner ear, but they are not converted into nerve signals that are interpreted by the brain as sounds.
Sensorineural deafness results from damage to the neural receptors of the inner ear (the hair cells, organ of Corti), the nerve pathways to the brain (notably the auditory nerve), or the area of the brain that receives sound information.
Sensorineural Deafness
Hearing loss or impairment due to a lesion or defect of the cochlea or the acoustic nerve
Sensory ...
Ocular Albinism-sensorineural Deafness [syndrome]
RPE
Retinal Pigment Epithelium ...
Hypoparathyroidism, sensorineural deafness, and renal disease
HDR syndrome
Nephrosis, nerve deafness, and hypoparathyroidism
None ...
Type 4 also involves sensorineural deafness.
Bartter Syndrome type 4A: Bartter syndrome is a rare disorder where abnormal kidney metabolism results in low blood acidity an potassium levels. Type 4A also involves sensorineural deafness.
Alport syndrome (AS) is an inherited disease characterised by glomerular nephropathy with hematuria, progressing to end-stage renal disease, associated with sensorineural deafness.
HDR syndrome: The syndrome of familial Hypoparathyroidism, sensorineural Deafness, and Renal dysplasia. It is inherited as an autosomal dominant trait and caused by haploinsufficiency of the GATA3 gene in chromosome 10p.
(Remember old age and earwax are much more common causes of deafness.) The type of deafness caused is called sensorineural deafness and means the nerve for hearing (the acoustic nerve) is damaged.
"Fountain's syndrome: mental retardation, sensorineural deafness, skeletal abnormalities, and coarse face with full lips". J Med Genet 26 (11): 722-4. PMID 2585470.
Fryns JP, Dereymaeker A, Hoefnagels M, Van den Berghe H (1987).
Axial T1-weighted MR images through temporal bones in a patient with left-sided sensorineural deafness: strongly enhancing area in the left vestibulum (a, arrow); compare with the right vestibulum (b, arrowhead).
Usher's syndrome n. An inherited syndrome characterized by sensorineural deafness and retinitis ... Genes associated with Usher syndrome. 5 Prospects for gene ...
Full article ...
Pendred’s syndrome: Causes 10% of cases of sensorineural deafness, with patients demonstrating goitre (enlargement of thyroid gland).
Electronic devices implanted beneath the skin with electrodes to the cochlear nerve to create sound sensation in persons with sensorineural deafness.
Latest Medical News ...
Mutations to the V-ATPase 'a4' or 'B1' isoforms result in distal renal tubular acidosis, a condition that leads to metabolic acidosis, in some cases with sensorineural deafness.
Cochlear Implant
A device consisting of microelectrodes that deliver electrical stimuli directly to the auditory nerve when surgically implanted into the cochlea, enabling a person with sensorineural deafness to hear. Also called "artificial ear." ...
 See also: Deafness, Symptom, Hearing Loss, Deficiency, Cancer
  
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